Diagnostic criteria for Behçet disease
Criterion | Required features |
---|---|
Recurrent oral ulceration | Aphthous (idiopathic) ulceration, observed by the physician or patient, with at least 3 episodes in any 12-month period |
Plus any two of the following: | |
Recurrent genital ulceration | Aphthous ulceration or scarring, observed by the physician or patient |
Eye lesions | Anterior or posterior uveitis or cells in the vitreous on slit-lamp examination; or retinal vasculitis documented by an ophthalmologist |
Skin lesions | Erythema nodosum-like lesions observed by the physician or patient Papulopustular skin lesions or pseudofolliculitis with characteristic acneiform nodules observed by the physician |
Pathergy test | Interpreted at 24 to 48 hours by the physician |
Reprinted from International Study Group for Behçet’s Disease. Criteria for diagnosis of Behçet’s disease. Lancet 1990; 335:1078–1080, copyright 1990, with permission from Elsevier, http://www.sciencedirect.com/science/journal/01406736?sdc=1.