Causes of primary and secondary distal renal tubular acidosis
Primary distal renal tubular acidosis Sporadic (idiopathic) Inherited (due to a congenital mutation) |
Secondary distal renal tubular acidosis Hypergammaglobulinemia Autoimmune disorders (eg, lupus erythmatosus, Sjögren syndrome, rheumatoid arthritis) Chronic renal allograft rejection Obstructive uropathy Medullary sponge kidney Autoimmune hepatitis Primary biliary cholangitis Lithium, amphotericin B, ifosfamide Sickle cell anemia |
Based on information in reference 2.