TABLE 2

Causes of primary and secondary distal renal tubular acidosis

Primary distal renal tubular acidosis
Sporadic (idiopathic)
Inherited (due to a congenital mutation)
Secondary distal renal tubular acidosis
Hypergammaglobulinemia
Autoimmune disorders (eg, lupus erythmatosus, Sjögren syndrome, rheumatoid arthritis)
Chronic renal allograft rejection
Obstructive uropathy
Medullary sponge kidney
Autoimmune hepatitis
Primary biliary cholangitis
Lithium, amphotericin B, ifosfamide
Sickle cell anemia
  • Based on information in reference 2.