TABLE 1

Etiology of portal hypertension

Presinusoidal causes
Idiopathic noncirrhotic portal hypertension
Biliary diseases (primary biliary cirrhosis, primary sclerosing cholangitis)
Neoplastic and nonneoplastic occlusion of the portal vein
Schistosomiasis
Polycystic disease
Arteriovenous fistulas
Congenital hepatic fibrosis
Sinusoidal causes
Drug-induced
Alcoholic liver damage
Nonalcoholic steatohepatitis
Viral hepatitis
Amyloid
Infiltrative diseases
Visceral leishmaniasis
Gaucher disease
Acute fatty liver of pregnancy
Postsinusoidal causes
Budd-Chiari syndrome
Veno-occlusive disease
Hypervitaminosis A
Primary vascular malignancies
Epithelioid hemangioendothelioma and angiosarcoma